Subtypes

Polysplenia syndrome with complete AV canal

May Cause

Abnormal position of the heart

Biliary system abnormality

Congenital biliary tract abnormality

Congenital heart disease

Congenital renal cystic disease

Congenital renal or ureteral anomaly

Dextrocardia

Esophageal atresia

Intestinal malrotation

Marked cyanosis in first week of life

Ovarian cyst

Ovarian tumor

Pancreatic dysplasia

Renal cystic disease

Situs ambiguus

Small or nonvisualized spleen

Tracheoesophageal fistula

Venous anomaly