Oculo-oto-dental syndrome

Otodental syndrome, also known as otodental dysplasia, is an exceptionally rare disease that is distinguished by a specific phenotype known as globodontia, that in rare cases can be associated with eye coloboma and high frequency hearing loss. Globodontia is an abnormal condition that can occur in both the primary and secondary dentition, except for the incisors which are normal in shape and size. [Source: Wikipedia ]

Synonyms
Oculootodental syndrome
May Cause
Coloboma