Byler disease

Biliary atresia, also known as extrahepatic ductopenia and progressive obliterative cholangiopathy, is a childhood disease of the liver in which one or more bile ducts are abnormally narrow, blocked, or absent. It can be congenital or acquired. [Source: Wikipedia ]

Synonyms
FIC1 deficiency
PFIC1
Progressive familial intrahepatic cholestasis type 1
Is A
Progressive familial intrahepatic cholestasis
May Cause
Cirrhosis
Liver failure