Gamuts

Pancreatic dysplasia

Renal–hepatic–pancreatic dysplasia is an autosomal recessive congenital disorder characterized by pancreatic fibrosis, renal dysplasia and hepatic dysgenesis. It is usually fatal soon after birth.An association with NPHP3 has been described. [Source: Wikipedia ]

Synonyms
Dysplasia of pancreas
Pancreas dysplasia
Subtypes
Polycystic pancreatic dysplasia
May Be Caused by
Agenesis of pancreas
Asphyxiating thoracic dysplasia
Cumming syndrome
Ellis-van Creveld syndrome
Familial renal-hepatic-pancreatic dysplasia
Meckel syndrome
Polysplenia syndrome
Short rib-polydactyly syndrome type 1
Short rib-polydactyly syndrome type 2
Shwachman–Diamond syndrome
Zellweger syndrome
Synonyms
Dysplasia of pancreas
Pancreas dysplasia
Subtypes
Polycystic pancreatic dysplasia
May Be Caused by
Agenesis of pancreas
Asphyxiating thoracic dysplasia
Cumming syndrome
Ellis-van Creveld syndrome
Familial renal-hepatic-pancreatic dysplasia
Meckel syndrome
Polysplenia syndrome
Short rib-polydactyly syndrome type 1
Short rib-polydactyly syndrome type 2
Shwachman–Diamond syndrome
Zellweger syndrome


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