Gamuts
Tricuspid atresia
OrphaNet reference
Tricuspid atresia
Subtypes
Tricuspid atresia and transposition of great vessels with no PS
Tricuspid atresia with pulmonary atresia
Tricuspid atresia with pulmonary stenosis
Tricuspid atresia with transposition of great vessels
Tricuspid atresia without PS
Tricuspid atresia without pulmonary stenosis
Tricuspid atresia without transposition
May Cause
Cardiomegaly in childhood
Congenital heart disease with anterior right aortic arch
Generalized pulmonary arterial hypovascularity
Heart failure in childhood
Late onset of cyanosis in neonatal congenital heart disease
Left atrial enlargement
Left ventricular enlargement
Patchy liver
Right atrial enlargement
Right-to-left atrial shunt
Right-to-left shunt or admixture lesion in congenital heart disease
Systemic-to-pulmonary vascular shunt
May Be Caused by
Robinow syndrome
Werner syndrome