Gamuts

Hypoplastic left heart syndrome

Hypoplastic left heart syndrome (HLHS) is a rare congenital heart defect in which the left side of the heart is severely underdeveloped. It may affect the left ventricle, aorta, aortic valve, or mitral valve. [Source: Wikipedia ]

OrphaNet reference
Hypoplastic left heart syndrome 
Subtypes
Aortic arch atresia with ASD
Aortic arch atresia with PDA
Aortic arch stenosis with ASD
Aortic arch stenosis with PDA
Aortic atresia with ASD
Aortic atresia with PDA
Aortic stenosis with ASD
Aortic stenosis with PDA
Mitral atresia with ASD
Mitral atresia with PDA
Mitral stenosis with ASD
Mitral stenosis with PDA
May Cause
Cardiomegaly
Cardiomegaly in childhood
Diaphragmatic hernia
Enlarged pulmonary veins
Heart failure
Heart failure in childhood
Heart failure in the first month of life
Heart failure in the first week of life
Large main pulmonary artery
Lymphedema
Marked cyanosis in first week of life
Pulmonary hypertension
Pulmonary venous hypertension
Right atrial enlargement
Right ventricular enlargement
Right-to-left shunt at ductus level
Small aortic arch
Small ascending aorta
May Be Caused by
Fanconi anemia

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