Hyperimmunoglobulinemia E syndrome

Hyperimmunoglobulinemia E syndrome (HIES), of which the autosomal dominant form is called Job's syndrome or Buckley syndrome, is a heterogeneous group of immune disorders. Job's is also very rare at about 300 cases currently in the literature. [Source: Wikipedia ]

Synonyms
Buckley syndrome
Hyper-IgE syndrome
Hyperimmunoglobulin E syndrome
Job syndrome
May Cause
Arterial aneurysm
Craniosynostosis
Delayed tooth eruption
Eczema
Immune disorder
Mastoiditis
Pneumatocele
Stomatitis
Buckley syndrome
Hyper-IgE syndrome
Hyperimmunoglobulin E syndrome
Job syndrome