Periauricular pits

A preauricular sinus is a common congenital malformation characterized by a nodule, dent or dimple located anywhere adjacent to the external ear. Frequency of preauricular sinus differs depending the population: 0.1–0.9% in the US, 0.9% in the UK, and 4–10% in Asia and parts of Africa.Preauricular sinuses are inherited features, and most often appear unilaterally. [Source: Wikipedia ]

May Be Caused by

Acrocallosal syndrome

Antley-Bixler syndrome

Asymmetric crying facies

Atypical osteopetrosis and posterior helical ear pits

Beckwith-Wiedemann syndrome

Branchiooculofacial syndrome

Branchiootorenal syndrome

Burn-McKeown syndrome

Carpenter syndrome

Cat-eye syndrome

Cerebro-costo-mandibular syndrome

Chromosome syndrome

Coffin-Siris syndrome

Da Silva syndrome

Familial posterior helical ear pits

Floating-harbor syndrome

Frontonasal dysplasia

Jones-Waldman syndrome

Kaufman oculocerebrofacial syndrome

Lenz microphthalmia syndrome

Nager acrofacial dysostosis

Oculo-auriculo-vertebral spectrum

Renal tubular dysgenesis-absent nipples syndrome

Townes-Brocks syndrome

Treacher Collins syndrome