Gamuts

Uhl anomaly

The Uhl anomaly is a partial or total loss of the myocardial muscle in the right ventricle. A congenital heart disease, it is very rare: fewer than 100 cases in 1900–1993.It was first described in 1952 by Dr. [Source: Wikipedia ]

Synonyms
Parchment RV
OrphaNet reference
Uhl anomaly 
May Cause
Cardiomegaly in childhood
Congenital heart disease
Congenital heart disease with decreased pulmonary vascularity
Generalized pulmonary arterial hypovascularity
Heart failure in childhood
Heart failure in the first month of life
Right atrial enlargement
Right ventricular enlargement
Right-to-left atrial shunt
Synonyms
Parchment RV
OrphaNet reference
Uhl anomaly 
May Cause
Cardiomegaly in childhood
Congenital heart disease
Congenital heart disease with decreased pulmonary vascularity
Generalized pulmonary arterial hypovascularity
Heart failure in childhood
Heart failure in the first month of life
Right atrial enlargement
Right ventricular enlargement
Right-to-left atrial shunt


Copyright © 2025, Charles E. Kahn, Jr., MD, MS
ALL RIGHTS RESERVED
About "Gamuts"

Quiz